3
22
Table 7. Lymphocyte Phenotype Classification
of SCID
24-26
Well-Defined Syndromes with Immunodeficiency
27-29
Predominantly Antibody Deficiencies
29
Table 8. Assessing Serotype-specific Responses
to Pneumococcal Capsular Polysaccharides
30-32
Diseases of Immune Dysregulation
30
Figure 3. Diagnosis of Diseases of Immune
Dysregulation
33-36
Phagocytic Cell Defects
33
Figure 4. Diagnosis of Phagocyte Defects
37-40
Defects of Innate Immunity
37
Figure 5. Diagnosis of Innate Immune Defects
41-45
Autoinflammatory Disorders
44-45
Figure 6. Diagnosis of Autoinflammatory
Syndromes
46
Complement Deficiencies
46
Anti-Cytokine Autoantibodies
47
Table 9. Summary of Screening Laboratory Findings
and Diagnosis of Complement Deficiencies
48
Table 10. Clinical Associations with Complement
Deficiency
49-60
Table 11. Classification of Primary
Immunodeficiencies