17
Î Patients with Schnitzler syndrome caused by an IgM monoclonal
gammopathy present with nonpruritic urticaria (that spares the face),
bone pain, and intermittent fever. (D)
Table 7. Very Rare Mimickers of Urticaria, Angioedema,
or Both
Acute hemorrhagic edema of childhood
Acute idiopathic scrotal edema of childhood
Angiolymphoid hyperplasia with eosinophilia
Blepharochalasis
Cheilitis glandularis
Cryopyrinopathies
Drug-related rash with eosinophilia and systemic symptoms (DRESS)
Factor I deficiency
Gleich syndrome
HES
Kimura disease
Melkersson-Rosenthal syndrome
Romana sign (trypanosomiasis)
Schnitzler syndrome
Schulman syndrome
Still disease
TRAPS
Well syndrome
