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Table 4. Common and Less/uncommon Urticaria
Angioedema or Urticaria-like Dermatoses
Common Less Common or Uncommon
Anaphylaxis Angiolymphoid hyperplasia with
eosinophilia
Atopic dermatitis Autoimmune progesterone-associated
dermatoses
Autoinflammatory syndromes:
Familial cold-autoinflammatory syndrome
Muckle-Wells, NOMID, Hyper-IgD
syndrome, TRAPS, PFAPA, PAPA, FMF
Autoimmune thyroid disease Blepharochalasis
Bullous pemphigoid Cheilitis glandularis
C1-inhibitor deficiencies Cheilitis granulomatosa
Contact dermatitis Cryoglobulinemia
Contact urticaria Drug-related eosinophilia with systemic
symptoms
Cutaneous and systemic lupus
erythematosus
Episodic angioedema with eosinophilia
Cutaneous mastocytosis Estrogen-induced angioedema
Dermatitis herpetiformis Complement factor I deficiency
Erythema multiforme (infection, drug ) HES
Exacerbation of physical urticaria Schnitzler syndrome/malignancies
Food/insect allergies Systemic mastocytosis (SM)
Adverse medication reactions Urticaria-like dermatoses of pregnancy
• Angioedema with ACE inhibitors • Gestational pemphigoid
• Fixed drug eruptions • PUPPS, prurigo of pregnancy
Parasite/bacterial infections Well syndrome
Polymorphous light eruption
Recall urticaria
Scabies, insect bites
Urticarial Vasculitis (e.g., hepatitis)
Viral infections
