61
Table 30. Double-Chambered Right Ventricle: Routine Follow-
Up and Testing Intervals
Type of Follow-Up
or Testing
Physiological
Stage A* (mo)
Physiological
Stage B* (mo)
Physiological
Stage C* (mo)
Physiological
Stage D* (mo)
Outpatient ACHD
cardiologist
24–36 24
6–12
3–6
Electrocardiogram 24–36 24
12 12
Transthoracic
echocardiogram
24–36 24 12 6–12
For recommendations about timing of CMR and CT imaging, see Section 4.3.3 supportive text
for recommendation #2.
Modified with permission from Stout et al. Copyright © 2018 American Heart Association, Inc.
and American College of Cardiolog y Foundation.
* See Section 2.2 for details on the ACHD anatomic and physiological classification system.
ACHD indicates adult congenital heart disease; CMR, cardiovascular magnetic resonance; and
CT, computed tomography.
4.3.4. Isolated Branch Pulmonary Artery Stenosis
COR LOE
Recommendations
Diagnostic
1 B-NR
1. In adults with peripheral or branch PA stenosis,
echocardiography and cross-sectional imaging (cardiac CT or
CMR) are recommended to evaluate RV pressure and systolic
function, degree of tricuspid regurgitation, and degree and
location of stenosis.
erapeutic
1 B-NR
2. In adults with symptoms related to peripheral or branch PA
stenosis, pulmonary branch balloon angioplasty and/or stent
implantation is recommended to improve hemodynamics and
symptoms.
2a B-NR
3. In asymptomatic adults with isolated peripheral PA
stenosis* and any of the following—RV hypertension that
is more than half the systemic pressure, RV dysfunction,
moderate or greater degree of tricuspid regurgitation, or
worsening exercise performance—pulmonary branch balloon
angioplasty and stent implantation can be useful to improve
hemodynamics, reduce tricuspid regurgitation, and improve
pulmonary blood flow.
* Angiographic narrowing and/or asymmetric pulmonary blood flow with a reduction >10%
in expected perfusion to the affected lung.
