60
Specific Conditions
Table 29. Isolated Pulmonary Regurgitation After Repair of
Pulmonary Stenosis: Routine Follow-Up and Testing
Intervals
Type of Follow-Up
or Testing
Physiological
Stage A* (mo)
Physiological
Stage B* (mo)
Physiological
Stage C* (mo)
Physiological
Stage D* (mo)
Outpatient ACHD
cardiologist
36–60 24
6–12
3–6
Electrocardiogram 36–60 24
12 12
Transthoracic
echocardiogram
36–60 24 12 12
For recommendations about timing of CMR imaging, see Section 4.3.2.1 supportive text for
recommendation #1.
Modified with permission from Stout et al. Copyright © 2018 American Heart Association, Inc.
and American College of Cardiolog y Foundation.
* See Section 2.2 for details on the ACHD anatomic and physiological classification system.
ACHD indicates adult congenital heart disease; and CMR, cardiovascular magnetic resonance.
4.3.3. Management of Double-Chambered Right Ventricle
COR LOE
Recommendations
Diagnostic
2a C-LD
1. In adults with RV dysfunction or symptoms attributed to
DCRV, cardiac catheterization is reasonable to characterize
anatomy and severity.
2a C-EO
2. In adults with DCRV and moderate or greater RVOT
obstruction, diagnostic assessment with CMR (or, if
contraindicated, cardiac CT) can be beneficial to characterize
the anatomy.*
erapeutic
1 C-LD
3. In adults with DCRV, moderate or greater RVOT
obstruction, and otherwise unexplained symptoms of heart
failure, cyanosis, or exercise limitation, surgical repair is
recommended to improve symptoms.
2a C-LD
4. In asymptomatic adults with DCRV and severe RVOT
obstruction, surgical repair is reasonable to prevent symptoms
and adverse RV remodeling.
* Table 27 delineates levels of severity of RVOT obstruction and their related
echocardiographic parameters.
