46
Specific Conditions
Table 19. Cor Triatriatum Sinister: Routine Follow-Up and
Testing Intervals
Type of Follow-Up
or Testing
Physiological
Stage A* (mo)
Physiological
Stage B* (mo)
Physiological
Stage C* (mo)
Physiological
Stage D* (mo)
Outpatient ACHD
cardiologist
36–60 12–24 6–12 3–6
Electrocardiogram 36–60 12–24
6–12 3–6
Transthoracic
echocardiogram
36–60 12–24 12 12
For recommendations about timing of CMR and CT angiography, see Section 4.2.1 supportive
text for recommendations #1 and #2.
* See Section 2.2 for details on the ACHD anatomic and physiological classification system.
ACHD indicates adult congenital heart disease, CMR, cardiovascular magnetic resonance; and
CT, computed tomography.
4.2.1. Cor Triatriatum Sinister
COR LOE
Recommendations
erapeutic
1 B-NR
3. In adults with unrepaired cor triatriatum sinister and
symptoms attributable to membrane obstruction, surgical
resection is recommended to reduce the consequences of left
atrial hypertension.
1 C-LD
4. In adults with unrepaired cor triatriatum sinister and
atrial fibrillation or atrial flutter, prior stroke, or left atrial
thrombus, chronic anticoagulation is recommended to
prevent embolic stroke, whether or not conventional
thromboembolic risk factors are present.
2a C-LD
5. In asymptomatic adults with unrepaired cor triatriatum sinister
and severe membrane obstruction, surgical resection can be
useful to prevent the sequelae of left atrial hypertension.
2a C-LD
6. In adults with unrepaired cor triatriatum sinister and atrial
fibrillation or atrial flutter, a rhythm control strateg y can be
beneficial to avoid clinical decompensation.
2b C-LD
7. In highly symptomatic adults with unrepaired cor triatriatum
sinister, significant membrane obstruction, and elevated
operative risk,* catheter-based intervention may be
considered as a bridge to surgical resection.
* For example, decompensated heart failure, severe pulmonary hypertension, or pregnancy
(see supportive text for details).
(cont'd)
