4
Definitions and Classifications
Table 4. ACHD AP Classification (CHD Anatomy +
Physiological Stage = ACHD AP Classification)
Congenital Heart Disease Anatomy
III: Great Complexity (or Complex)
Double-outlet ventricle
Fontan physiolog y
Interrupted aortic arch
Pulmonary atresia (all forms, including tetralog y of Fallot with pulmonary atresia)
Single-ventricle anatomy (including double-inlet le ventricle, tricuspid/mitral atresia,
hypoplastic le heart, any other anatomic abnormality with a functionally single ventricle)
Congenitally corrected TGA (CCTGA, levo-TGA)
Dextro-TGA aer atrial switch (Mustard/Senning ) operation
Dextro-TGA aer Rastelli operation
Truncus arteriosus
Unrepaired or partially palliated cyanotic congenital heart defect
Physiological Stage
Stage A
No cardiac symptoms
No hemodynamic or anatomic sequelae
No sustained arrhythmias*
Normal exercise capacity*
Normal pulmonary pressure
Stage B
Arrhythmia* not requiring new treatment or a change in therapy in the past 12 months
Mild native valve dysfunction* or prosthetic valve with normal function
Mild ventricular dysfunction
Mild ventricular enlargement
Presence of a permanent pacemaker or ICD, without need for ICD therapy in the past
12 months
Trivial or small shunt* (not hemodynamically significant)
(cont'd)
