3
Definitions and
Classifications
Note: The numbering of the following tables and figures may differ from that of
the Clinical Practice Guideline.
Colors in tables and figures correspond to Class of Recommendations and
Level of Evidence tables on pages 92–93.
Table 4. ACHD AP Classification (CHD Anatomy +
Physiological Stage = ACHD AP Classification)
Congenital Heart Disease Anatomy
I: Simple
Ostium secundum ASD
Patent ductus arteriosus
Ventricular septal defect
Pulmonic stenosis
II: Moderate Complexity
Anomalous aortic origin of a coronary artery from the opposite sinus
Anomalous coronary artery arising from the pulmonary artery
Anomalous pulmonary venous connection, partial or total
Atrioventricular septal defect (partial or complete)
Congenital aortic valve disease
Congenital mitral valve disease
Coarctation of the aorta
Cor triatriatum sinister
Dextro-TGA aer arterial switch operation
Ebstein anomaly
Infundibular right ventricular outflow obstruction/double-chamber right ventricle
Peripheral pulmonary artery stenosis
Sinus venosus defect
Subvalvular aortic stenosis (excluding hypertrophic cardiomyopathy, which these
guidelines do not address)
Supravalvar aortic stenosis
Tetralog y of Fallot
Vascular ring or sling
2.2 The ACHD Anatomic and Physiological Classification
System
