10
Figure 1. Rhythm management and CIED in patients with
DMD, BMD, or recessive LGMD2 and left ventricular
dysfunction
Patient with DMD,
BMD, or LGMD2
a
YES
YES
YES
YES
NYHA class II to IV
ICD concordant with
patient goals of care
and clinical status
LVEF ≤35% on GDMT
LBBB QRS
≥150 ms and/or
RV pacing ≥40%
NO
NO
NO
NO
Cardiac evaluation
b
(1)
CRT-D
(2a)
Duchenne, Becker, and Recessive Limb-girdle
Muscular Dystrophies
