9
Atrial arrhythmias in Duchenne, Becker, and recessive limb-
girdle muscular dystrophies
COR LOE Recommendation
1 B-NR 1. In patients with DMD, BMD, or LGMD2, anticoagulation
according to established guidelines and clinical context is
recommended for AF or atrial flutter (AFL) taking into
consideration the risks of thromboembolism and bleeding
on oral anticoagulation.
VAs, sudden cardiac death, and use of ICDs in Duchenne,
Becker, and recessive limb-girdle muscular dystrophies
COR LOE Recommendations
1 B-NR 1. In patients with DMD, BMD, or LGMD2 with
spontaneously occurring hemodynamically significant
sustained ventricular tachycardia (VT) or ventricular
fibrillation (VF) ICD therapy is indicated if concordant with
the patient's goals of care and clinical status.
2a B-NR 2. In patients with DMD, BMD, or LGMD2 with an LVEF
≤35% despite GDMT, ICD therapy is reasonable if
concordant with the patient's goals of care and clinical status.
