18
Figure 2. Rhythm management and CIED implantation in
patients with DM1 or DM2 with normal ventricular
function and with focus on the risk stratification
for the prevention of sudden death
Patient with DM1 or DM2
a
YES
YES
YES YES
YES
PR ≥240 ms, QRS
≥120 ms, or 2nd or 3rd
degree AV block
Symptoms of
bradycardia
Inducible
VT/VF
HV
≥70 ms
NO
NO
NO
NO
NO
NO
Cardiac evaluation
b
(1)
ICD
(1)
EP study
c
(2b)
EP study
c
(2a)
Symptoms of VT
and nondiagnostic
noninvasive testing
Mild to moderate
conduction disorder
d
and nondiagnostic
noninvasive testing
e
Myotonic Dystrophy Types 1 and 2
Sinus node
dysfunction or AV
block on noninvasive
testing
f
