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Sarcoidosis

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14 Diagnosis Table 4. Key Differential Diagnoses for Sarcoidosis within Individual Organ Systems Organ System Noninfectious Differential Diagnoses Infectious Differential Diagnoses Central nervous system IgG4-related disease Chronic variable immunodeficiency Rosai-Dorfman disease Histiocytoses • Histiocytosis X • Erdheim-Chester Lymphomatoid granulomatosis Granulomatosis with polyangiitis Rheumatoid nodules Amyloidosis Cholesterol granuloma Foreign body Drugs/toxins/heavy metals Sarcoid-like reaction to tumor CNS malignancies ranging from glioblastoma to lymphoma Bacteria • Tuberculosis • Brucella Fungi • Aspergillus • Coccidioidomycosis • Cryptococcosis Parasites • Amoeba • Toxoplasmosis • Schistosomiasis • Taenia solium • Echinococcus • Paragonimiasis Viruses • Varicella zoster • Herpes simplex Eyes Inflammatory bowel disease ANCA vasculitides Vogt-Koyanagi-Harada disease Blau syndrome Parinaud oculoglandular syndrome • Bartonella • Francisella Bacteria • Tuberculosis • Syphilis Viruses Cytomegalovirus • Varicella zoster Toxoplasmosis Sinonasal Granulomatosis polyangiitis Eosinophilic granulomatosis with polyangiitis Cholesterol granuloma NK/T-cell lymphoma Foreign body Drugs/toxins • Cocaine • Narcotics Bacteria • Tuberculosis • Atypical Mycobacteria • Klebsiella Rhinoscleromatis • Syphilis Fungi • Aspergillus flavus • Histoplasmosis Parasites • Leishmaniasis • Rhinosporidiosis

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