66
Specific Conditions
Table 33. Published Risk Scores for Calculating Risk for
Sustained Ventricular Tachycardia/Sudden Cardiac
Death in Repaired Tetralogy of Fallot
PREVENTION-ACHD Brompton, UK
Case-control design Observational design
Outcome: SCD Outcome: SCD, sustained VT, resuscitated VF
783 patients 550 patients
8 events 29 events
Risk factor* Points Risk factor
†
Points
Coronary artery disease 1 RV LGE extent
NYHA II–III symptoms 1 Moderate 22
Supraventricular tachycardia 1 Severe 24
Systemic EF <40% 1 LV LGE present 11
Subpulmonary EF <40% 1 RVEF
QRS duration ≥120 ms 1 36%–47% 8
QT dispersion ≥70 ms 1 ≤35% 16
LVEF
36%–55% 5
≤35% 17
Peak VO
2
≤17 mL/kg/m
2
9
BNP ≥127 ng/L 9
Akinetic RVOT length ≥55 mm 9
RV pressure ≥47 mm Hg 5
Total score
Annual
event rate Total score
Annual
event rate
0–2 <1% 0–20 0.20%
3 1%–2% 21–39 0.90%
4 3%–4% ≥40 3.70%
5 5%–10%
6 11%–25%
7 >25%
* Echocardiographic values
†
CMR values
