90
Specific Conditions
Table 45. Anomalous Aortic Origin of a Coronary Artery:
Routine Follow-Up and Testing Intervals
Type of Follow-
Up or Testing
Physiological
Stage A* (mo)
Physiological
Stage B* (mo)
Physiological
Stage C* (mo)
Physiological
Stage D* (mo)
Outpatient ACHD
cardiologist
24–36 12
12
12
Electrocardiogram 24–36 12
12 12
Transthoracic
echocardiogram
24–36 24
12 12
For recommendations on routine CT and MR angiography, see supportive text for
recommendations #1 and #2.
* See Section 2.2 for details on the ACHD anatomic and physiological classification system.
ACHD indicates adult congenital heart disease; CT, computed tomography; and MR,
magnetic resonance.
4.5.2. Anomalous Coronary Artery Arising From the
Pulmonary Artery
COR LOE Recommendations
1 B-NR
1. In adults with an anomalous left coronary artery arising from
the PA, surgery is recommended to improve cardiac function
and reduce the risk for myocardial ischemia.
1 B-NR
2. In symptomatic adults with an anomalous right coronary
artery arising from the PA and with evidence of ischemia,
surgery is recommended to reduce ischemia, to reduce the
risk for SCD, and to improve cardiac function.
2b B-NR
3. In asymptomatic adults with an anomalous right coronary
artery arising from the PA and without evidence of cardiac
dysfunction or ischemia, surgery may be considered to avoid
the development of cardiac dysfunction.
