36
Figure 4. Rhythm management and CIED implantation in
patients with mitochondrial myopathies including FA
Patient with mitochondrial
myopathy or FA
a
YES
YES
YES
YES
LVEF ≤35%
on GDMT
NO
Cardiac evaluation
b
(1)
ICD
(2a)
CRT-P
(2a)
CRT-D
(2a)
NO
NO
NO
NO
ICD
concordant with
patient goals of
care and clinical
status
ICD
concordant with
patient goals of
care and clinical
status
LBBB
(QRS ≥150 ms)
and/or RV
pacing ≥40%
NYHA
class II to IV
YES
Mitochondrial Myopathies Including Friedreich Ataxia
