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is resource is for informational purposes only, intended as a quick-reference tool based on the
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Source
Groh WJ, Bhakta D, Tomaselli GF, et al. 2022 HRS expert consensus statement
on evaluation and management of arrhythmic risk in neuromuscular disorders.
HeartRhythm. 2022;19(10):e61-e120. doi:10.1016/j.hrthm.2022.04.022
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Abbreviations
AD, autosomal dominant; AF, atrial fibrillation; AFL, atrial flutter; AR, autosomal
recessive; AV, atrioventricular; BMD, Becker muscular dystrophy; BPM, beats per minute;
CIED, cardiovascular implantable electronic device; CM, cardiomyopathy; CMR, cardiac
magnetic resonance imaging ; COR, class of recommendation; CRM, cardiac rhythm
management; CRT, cardiac resynchronization therapy; CRT-D, cardiac resynchronization
therapy with defibrillator; CRT-P, cardiac resynchronization therapy with pacemaker;
DM, myotonic dystrophy; DM1, myotonic dystrophy type 1; DM2, myotonic dystrophy
type 2; DMD, Duchenne muscular dystrophy; DMPK, myotonic dystrophy protein
kinase; DUX4, double homeobox 4; ECG, electrocardiogram; EDMD, Emery-Dreifuss
muscular dystrophy; EDMD1, Emery-Dreifuss muscular dystrophy type 1; EDMD2,
Emery-Dreifuss muscular dystrophy type 2; EDMD3, Emery-Dreifuss muscular dystrophy
type 3; EP, electrophysiological; FA, Friedreich ataxia; FSHD, facioscapulohumeral
muscular dystrophy; GDMT, guideline-directed medical therapy; HCM, hypertrophic
cardiomyopathy; ICD, implantable cardioverter-defibrillator; LBBB, le bundle branch
block; LGMD, limb-girdle muscular dystrophy; LGMD1B, limb-girdle muscular
dystrophy type 1B; LGMD2, limb-girdle muscular dystrophy type 2; LOE, level of
evidence; LVEF, le ventricular ejection fraction; mtDNA, mitochondrial DNA;
NMD, neuromuscular disorder; NYHA, New York Heart Association; PPM, permanent
pacemaker; RBBB, right bundle branch block; RCT, randomized controlled trial; RV,
right ventricular; VA, ventricular arrhythmia; VF, ventricular fibrillation; VT, ventricular
tachycardia; XL, X-linked; ZNF9, zinc finger 9