36
Treatment
Figure 18. Suggested Aortic Monitoring Protocol for Girls and
Women With Turner Syndrome Who Are ≥15 Years
of Age
≥15 y of age:
Cardiology Examination, TTE, CMR
No CoA, BAV, HTN
Repeat
examination
by cardiologist
+ TTE or MRI
every 5–10 y
(1)
ASI <2.0 cm/m
2
ASI 2.0–2.3 cm/m
2
ASI >2.3 cm/m
2
Low risk Moderate risk Moderate risk
Repeat
examination
by cardiologist
+ TTE or MRI
every 3–5 y
(1)
Repeat
examination
by cardiologist
+ TTE or MRI
every 1 y
(1)
* Surveillance frequency may vary depending on disease severity (ie, aortic valve
dysfunction, severity of coarctation obstruction, hypertension, and le ventricular
hypertrophy).