10
Figures
Figure 3. Schematic Pathway for Clinical Management of
Patients With IPF
Time
Patients should be made aware of available clinical
trials for possible enrollment at all stages.
Treatment Considerations
Pharmacological
• Nintedanib
• Pirfenidone
Nonpharmacological
• Oxygen supplementation
(if hypoxemic)
• Pulmonary rehabilitation
Comorbidities
• Pulmonary hypertension
• Gastroesophageal reflux
• Obstructive sleep apnea
• Lung cancer
Symptom Control
• Palliative care
If increased risk of mortality, evaluate
for lung transplantation at diagnosis
Diagnosis
of IPF
