2
Table of Contents
Page
4
Evidence Grades, Internet Resources for PIDDs
5
Abbreviations
6
Key Points
7
Diagnosis
7
General Considerations
8
Figure 1. General Approach for the Diagnosis of
Primary Immunodeficiency
9-10
Table 1. Characteristic Clinical Presentations of
Some Immunodeficiency Disorders
11
Table 2. Laboratory Tests of Immune Function
12
Table 3. Summary of Laboratory Findings in the
Diagnosis of Antibody Deficiencies
13
Treatment
14-16
Table 4. Summary of Therapeutic Considerations
for Primary Immunodeficiencies and their
Complications
16
Table 5. Regimens for Prophylaxis of Bacterial
Respiratory Tract Infections
17-48
Categories of PIDD
17
Figure 2. Diagnosis of Combined or Syndromic
Immunodeficiencies
15
Combined B- and T-Cell Immunodeficiencies
19-21
Table 6. Clinical and Laboratory Manifestations
of Selected Combined Immunodeficiencies and
Syndromes
